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Journal of IMAB - Annual Proceeding (Scientific Papers)
Publisher: Peytchinski, Gospodin Iliev
ISSN: 1312-773X (Online)
Issue: Volume 15, book 1, 2009
Subject Collection: Medicine
Page: 9 - 12
DOI: 10.5272/jimab.1512009_9
Online date:June 15, 2009
DIFFICULTIES IN THE ECHOCARDIOGRAPHIC DIAGNOSIS
OF BLAND-WHITE-GARLAND SYNDROME
P. Shivachev, Lachezar
Marinov
Department of Pediatrics
Medical University “Prof. Dr Paraskev Stoyanov”-Varna, Bulgaria
SUMMARY: The Bland-White-Garland Syndrome (BWG)
is a rare, but serious congenital cardiac anomaly, found in 1/300 000
life born children or is 0,25-0,5% of the congenital heart anomalies (CHA).
At the same time it is the most frequent congenital coronary anomaly –
90%. It is described for the first time in 1866, but the full clinical-anatomic
description is given from Bland, White and Garland in 1933, and that is
why it takes their names. It represents anomaly of the start of the left
coronary artery from the trunk of the pulmonary artery (ALKAPA), most
often from the left sinus with signs of myocardial ischemia in the relevant
zones. In evolution develop collaterals between both coronary arteries
and the syndrome of “stealing” because of the presence of significant
left-right shunt on vascular level. Connected to this there are two forms
of the disease: infantile and adult.
The aim of this report is to present the ECG and EchoCG results, clinical
manifestation and result of the held conservative and operative treatment
in three children, hospitalized in the clinic during the last years, establishing
diagnostic difficulties in the echocardiograph examination and specifying
of the type of the congenital cardiac malformation.
Key words:Bland-White-Garland syndrome, EchoCG, ECG,
clinical manifestation, outcome of the disease.
Page: 9-12; FULL TEXT PDF (456 KB)