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Journal of IMAB - Annual Proceeding (Scientific Papers)
Publisher: Peytchinski, Gospodin Iliev
ISSN: 1312 773X (Online)
Issue: 2010, vol. 16, book 4
DOI: 10.5272/jimab.1642010_10-13
Subject Collection:Oral and Dental Medicine
Page: 10 - 13
Online date: July 19, 2010
FIBROUS DYSPLASIA IN THE MAXILLO-MANDIBULAR REGION – case report
Radka Cholakova, P. Kanasirska*, N. Kanasirski, Ivan Chenchev, Atanaska Dinkova
Department of Oral Surgery, Faculty of Dental Medicin, *Department of Allergology, Physiotherapy and Clinical radiology, Medical University - Plovdiv, Bulgaria
ABSTRACT:
Craniofacial fibrous dysplasia is 1 of 3 types of fibrous dysplasia that can affect the bones of the craniofacial complex, including the mandible and maxilla.
Fibrous displasia is a skeletal developmental disorder of the bone-forming mesenchyme that manifests as a defect in osteoblastic differentiation and maturation.
It is a lesion of unknown etiology, uncertain pathogenesis, and diverse histopathology.
Fibrous dysplasia represents about 2, 5% of all bone tumors and over 7% of all benign tumours.
The aim of this article is to represent a rare case of bilateral fibrous dysplasia of the upper and lower jaws, in combination with Intellectual disability (previously called mental retardation). The clinical diagnostic approach including imaging studies: Orthopantomogram (OPG) and 3D tomography is described. Histological examination was also essential for obtaining a definitive diagnosis.
Key words: fibrous dysplasia, Lichtenstein-Jaffe’s disease, Maxillofacial, McCune-Albright’s disease, osteodystrophia fibrosa, osteitis fibrosa disseminata, monostotic form, polyostotic form, craniofacial form, cherubism, 3D tomography, Intellectual disability.
Page: 10-13; FULL TEXT PDF (207 KB) Abstract
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